Objective　To explore the clinical characteristics of Takayasu’s arteritis in children. Method　The clinical data of Takayasu’s arteritis in a child were analyzed, and the relevant literatures were reviewed. Results　The 7-year-old girl had recurrent fever of unknown causes, and the inflammatory indicators were significantly increased, and the anti-infection treatment was ineffective. PET-CT was performed and vasculitis was considered. After receiving glucocorticoid therapy, the patient's condition was recurrent, and angiography was performed to confirm the diagnosis of arteritis. Subsequently, the patient had surgical operation, and treated with glucocorticoids and cyclophosphamide, and no recurrence occurred. Conclusions For those with unexplained fever, accompanied by elevated inflammatory indicators and ineffective anti-infective treatment, clinician should be alert to the possibility of Takayasu’s arteritis. Early PET-CT examination and treatment by combination of glucocorticoid and cyclophosphamide after diagnosis can effectively improve the prognosis.