Hepatoblastoma (HB) is the most common malignant liver tumors among children. It typically begins with few symptoms, making it difficult to diagnose and treat. The number of HB cases has been on the rise in recent years, resulting in gradual development of the research on various aspects of the disease. This paper is a round-up of the etiology, pathological classification, clinical staging, prognostic factors and therapeutic principles of hepatoblastoma.