关键词: 婴儿型肝脏血管内皮细胞瘤；　心力衰竭；　临床特征

Abstract: Objective　To explore the clinical features, treatment and prognosis of infantile hepatic hemangioendothelioma (IHHE) with heart failure. Method　The clinical data of IHHE with heart failure in 2 infants were retrospectively analyzed, and relevant literature was reviewed. Results　In case 1 (female), her prenatal ultrasonography showed a heterogenous echogenicity in the left abdomen of the fetus and it was confirmed by magnetic resonance and CT on the 5th day after delivery, clinical appearance of cardiac failure on the 7th day. The resection was performed by surgical operation and the diagnosis of IHHE was confirmed by pathological examination on the 15th day after birth. Reexamination at age of 2 months showed no abnormality. Case 2 (male) was admitted to hospital on the 15th day of birth due to neonatal jaundice, and heart failure occurred rapidly. IHHE was diagnosed clinically by MRI and CT. Due to the rapid progression of the disease, the child died of preoperative decompensated heart failure and respiratory failure. Conclusion　The mortality of infantile IHHE with heart failure is high. Early recognition, early intervention and multidisciplinary intervention can improve the prognosis.

Key words: 　infantile hepatic hemangioendothelioma;　heart failure;　clinical characteristics