目的　探讨J波综合征的临床特征。方法　回顾分析1例因晕厥收治入院的J波综合征患儿的临床资料，并复 习相关文献。结果　男性患儿，10岁，无明显诱因出现晕厥。心电图提示J点抬高，呈Osbron波表现；彩色超声心动图示 心脏结构大致正常，左心室收缩功能正常；脑电图、头颅CT无异常。在随访过程中出现频繁晕厥，并伴有恶性心律失常表 现。结论　J波综合征患者是发生恶性心律失常及心源性猝死的高危人群。

　Objective　To explore clinical characteristics of J wave syndromes. Methods　Clinical data was retrospectively analyzed in a child with fainting and showing big J wave in ECG. Meanwhile, related literatures were reviewed. Results　A 10-year-old boy was admitted to hospital with fainting. ECG showed J point up, reflecting Osbron wave. There was no abnormality in EEG and cranial CT. Ultrasound cardiograph showed approximately normal heart structure and left ventricular systolic function. Fainting was frequently occurred during follow-up and accompanied by malignant arrhythmia. Conclusions　Patients with J wave syndromes has high risks of malignant arrhythmia and sudden cardiac death.