目的　探讨以发热、黄疸为首发症状的不完全川崎病（IKD）的临床特征。方法 回顾分析2例以发热、黄疸 为首发症状的不完全KD患儿的临床资料，并复习相关文献。结果 3岁9个月男性患儿及10岁女性患儿，以发热、皮肤黄染、 淋巴结肿大、球结膜充血为早期主要症状，均无皮疹，后期出现指端、肛周蜕皮，并冠状动脉扩张。其中男性患儿出现动眼 神经麻痹及丙种球蛋白抵抗，女性患儿出现KD休克综合征。结论 以发热、黄疸为首发症状的IKD患儿，可能因症状不 典型而致诊断延迟。

Objective　To?explore?the?clinical?features?of?incomplete?Kawasaki?disease?(IKD)?with?first?symptoms?of? fever?and?jaundice.?Method　The?clinical?data?of?incomplete?KD?with?the?first?symptoms?of?fever?and?jaundice?in?2?cases?were? retrospectively?analyzed,?and?relevant?literature?was?reviewed.?Results　In?two?patients?(3-year-?and?9-month-old?boy?and?a? 10-year-old?girl),?the?main?early?symptoms?were?fever,?yellowish?skin,?lymphadenopathy?and?bulbar?conjunctival?hyperemia,? and?no?rash.?They?presented?with?periungual?and?perianal?desquamation?and?coronary?artery?ectasia?at?the?later?stage.?The?boy? developed?oculomotor?palsy?and?gamma?globulin?resistance,?and?the?girl?developed?KD?shock?syndrome.?Conclusion　The diagnosis?in?IKD?children?with?fever?and?jaundice?as?the?first?symptoms?may?be?delayed?due?to?atypical?symptoms.