川崎病（KD）是儿童常见的急性血管炎，而川崎病休克综合征（KDSS）是KD少见而又严重的表现形式，近年 来逐渐引起临床医师的关注，因其可出现在疾病早期，病情进展迅速，并伴有多系统器官受累，早期诊断困难，极易漏诊 和误诊。本文综述了近年来KDSS诊断、早期识别、发病机制及治疗和预后等的研究进展。

Kawasaki disease (KD) is a common acute vasculitis in children, while Kawasaki disease shock syndrome (KDSS) is a rare and serious manifestation of KD. In recent years, KDSS has gradually attracted the attention of clinicians, because it can appear in the early stage of the disease, with rapid progression and multi-system organ involvement. Early diagnosis of KDSS is difficult and is very easy to miss diagnosis and misdiagnose. This article reviews the research progress of KDSS in the diagnosis, early recognition, pathogenesis, treatment and prognosis in recent years.