目的 分析三种不同手术方式在Carpentier C型三尖瓣下移畸形（EA）中的应用。方法 回顾分析2011年6 月至2017年8月接受手术的39例Carpentier C型EA患儿的临床资料。结果 共有39例Carpentier C型EA患儿，其中男18例、 女21例；中位年龄28.3（11.7~63.4）月；中位体质量12.6（8.7~19.2）kg。13例患儿行单一三尖瓣锥形重建术（A组），18 例行锥形重建联合双向腔肺分流术（B组），8例行单一双向腔肺分流术（C组）。三组之间术前青紫和心功能分级比例的差 异有统计学意义（P

Objective To explore the application of three different surgical methods in Carpentier C-type Ebstein’s anomaly (EA). Methods The clinical data of Carpentier C-type EA in 39 children who underwent surgery from June 2011 to August 2017 were retrospectively analyzed. Results A total of 39 children (18 boys and 21 girls) with Carpentier C-type EA were included. The median age was 28.3 (11.7-63.4) months and the median weight was 12.6 (8.7-19.2) kg. Among them, 13 patients underwent cone reconstruction (CR) surgery only (group A), 18 patients underwent CR combined with bidirectional cavo-pulmonary shunt (BCPS, group B), and 8 patients only underwent BCPS (group C). There were significant differences in the proportion of preoperative cyanosis and cardiac function classification among the three groups (P< 0 . 05 ). The children in group C had a higher proportion of preoperative cyanosis and worse cardiac function (grade Ⅲ and Ⅳ). The differences in the cardiopulmonary bypass (CPB) time, aortic cross-clamp (ACC) time, mechanical ventilation time, ICU stay time, postoperative hospital stay, incidence of low cardiac output syndrome, treatment cost during hospitalization and follow-up time among the three groups were statistically significant (P< 0 . 05 ). Pairwise comparisons showed that the CPB time, ACC time, mechanical ventilation time, ICU stay time, and postoperative hospital stay of group B were longer than those of group C, while the treatment cost during hospitalization of group C was higher than that of group A, and the differences were statistically significant (P