综合报道

胸膜肺母细胞瘤1例报告

  • 王贤书 ,
  • 杨志国 ,
  • 岳芳 ,
  • 高飞飞 ,
  • 陈志国
展开
  • 河北省儿童医院(河北石家庄 050031)

收稿日期: 2015-03-15

  网络出版日期: 2015-03-15

Pleuropulmonary blastoma: one case report

  • WANG Xianshu ,
  • YANG Zhiguo ,
  • YUE Fang ,
  • GAO Feifei ,
  • CHEN Zhiguo
Expand
  • Hebei Children’s Hospital, Shijiazhuang 050031, Hebei, China

Received date: 2015-03-15

  Online published: 2015-03-15

摘要

目的 探讨胸膜肺母细胞瘤的早期诊断及治疗。方法 回顾性分析1例由1型胸膜肺母细胞瘤逐渐进展为3型患儿的诊治过程。结果 患儿,男,生后18 d胸片未见明显异常;1岁时胸片示左肺近肺门处囊性占位,约5 cm×4 cm×4 cm,考虑为先天性肺囊性腺瘤样畸形,家长拒绝手术;3岁2个月,胸片及胸部CT提示左肺囊性实性占位,体积较前明显增大,背侧为实性,上部位巨大含气空腔;2个月后患儿出现呼吸喘憋,复查胸部CT示肿瘤完全实变,考虑胸膜肺母细胞瘤3型。手术切除后常规化疗,随访1年尚未复发。结论 1型胸膜肺母细胞瘤与先天性肺囊性腺瘤样畸形不宜鉴别,早期诊断及治疗可改善1型胸膜肺母细胞瘤的预后。

本文引用格式

王贤书 , 杨志国 , 岳芳 , 高飞飞 , 陈志国 . 胸膜肺母细胞瘤1例报告[J]. 临床儿科杂志, 2015 , 33(3) : 251 . DOI: 10.3969j.issn.1000-3606.2015.03.013

Abstract

Objective To investigate the early diagnosis and treatment of pleuropulmonary blastoma in children. Methods  The progress of pleuropulmonary blastoma from type 1 to type 3 was retrospectively analyzed. Results  The male infant had no obvious abnormality in chest X-ray at 18 days. At one year old, X-ray film of the chest showed cystic lesions near hilum of the left lung (about 5 cm × 4 cm × 4 cm). The congenital cystic adenomatoid malformation was considered and an operation resection was suggested. However, it had been rejected by his parents. At 3 years and 2 months old, chest X-ray and CT showed left lung had a solid cystic lesion, the volume was significantly enlarged, the back side was solid and the upper part had a large gas cavity. Two months later, the patient had asthmatic suffocation. The chest CT showed the tumor was completely solid. Pleuropulmonary blastoma type 3 was considered. The patient received the conventional chemotherapy after operation excision, and was followed up for 1 year. No recurrence was observed after the treatment. Conclusions  Type 1 pleuropulmonary blastoma and congenital cystic adenomatoid malformation are hard to be differentially diagnosed. Early diagnosis and treatment of type 1 pleuropulmonary blastoma can improve the prognosis.
文章导航

/