Journal of Clinical Pediatrics ›› 2025, Vol. 43 ›› Issue (10): 749-754.doi: 10.12372/jcp.2025.24e1413
• Original Article • Previous Articles Next Articles
ZHAO Xiaopei, XIAO Tingting, XU Meng()
Received:
2025-01-02
Accepted:
2025-05-15
Published:
2025-10-15
Online:
2025-09-29
Contact:
XU Meng
E-mail:xum@shchildren.com.cn
CLC Number:
ZHAO Xiaopei, XIAO Tingting, XU Meng. Clinical characteristics and prognostic analysis of partial anomalous pulmonary venous connection with intact atrial septum[J].Journal of Clinical Pediatrics, 2025, 43(10): 749-754.
Table 1
The intracardiac anatomical abnormalities of the children and their clinical manifestations at the visit"
患儿 | 类型 | 确诊方式 | 确诊时年龄 /月 | 性别 | 异位引流 的肺静脉 | 合并心 内畸形 | 三尖瓣反流压差/mmHg | 右房右 室增大 | 就诊时临床表现 |
---|---|---|---|---|---|---|---|---|---|
例1 | 心下型 | 超声心动图 | 92 | 女 | RIPV | 无 | 22 | 无 | 关节肿痛 |
例2 | 心上型 | 手术术中 | 101 | 女 | RSPV | 心脏占位 | 35 | 稍大 | 反复呼吸道感染/心脏占位 |
例3 | 心上型 | 超声心动图 | 6 | 女 | LSPV | 无 | 21 | 无 | 生长发育迟缓 |
例4 | 心上型 | 超声心动图 | 41 | 男 | RSPV | 无 | 25 | 无 | 生长发育迟缓 |
例5 | 心上型 | 心脏CTA | 81 | 女 | RSPV | 无 | 27 | 无 | 心脏杂音(II级) |
例6 | 心内型 | 心脏CTA | 5 | 女 | RSPV+RIPV | PDA+肺动脉吊带 | 55 | 增大 | 心脏杂音(III级)/反复喘息 |
例7 | 心上型 | 超声心动图 | 12 | 男 | LSPV | 无 | 22 | 无 | 不完全性右束支传导阻滞 |
例8 | 心上型 | 超声心动图 | 70 | 男 | LSPV | 无 | 24 | 无 | 室性期前收缩 |
例9 | 心下型 | 超声心动图 | 22 | 男 | RIPV | 右位心 | 33 | 稍大 | 右侧膈肌缺损 |
例10 | 心上型 | 超声心动图 | 36 | 男 | LSPV | 肺动脉狭窄 | 38 | 稍大 | 心脏杂音(III级) |
例11 | 心上型 | 超声心动图 | 36 | 男 | LSPV | 无 | 21 | 无 | 生长发育迟缓 |
例12 | 心上型 | 超声心动图 | 4 | 女 | LSPV+LIPV | 无 | 45 | 增大 | 左侧隔离肺 |
例13 | 心下型 | 心脏CTA | 60 | 男 | RIPV | 右位心 | 24 | 无 | 反复呼吸道感染 |
例14 | 心下型 | 超声心动图 | 24 | 女 | RIPV | 无 | 22 | 无 | 反复呼吸道感染 |
例15 | 心上型 | 超声心动图 | 30 | 女 | LSPV | 无 | 20 | 无 | 生长发育迟缓 |
例16 | 心内型 | 超声心动图 | 72 | 女 | RIPV | 无 | 24 | 无 | 胸闷/胸痛 |
Table 2
Anomalous pulmonary venous drainage pathway and surgical data of the children"
患儿 | 肺静脉异位引流路径 | 手术方式 | 合并畸形手术 | 术后1个月随访 | 术后1年随访 |
---|---|---|---|---|---|
例1 | RIPV-IVC-RA | 暂未手术 | / | / | / |
例2 | RSPV-SVC-RA | 人造ASD+单补片法 | 心脏占位切除 | 无殊 | 无殊 |
例3 | LSPV-LINV-SVC | 暂未手术 | / | / | / |
例4 | RSPV-SVC-RA | 人造ASD+单补片法 | 无 | 上腔静脉流速(1.4 m·s-1) | 上腔静脉流速(1.2 m·s-1) |
例5 | RSPV-SVC-RA | 人造ASD+单补片法 | 无 | 心电图:T波改变 | 心电图正常 |
例6 | RSPV+RIPV-RA | 人造ASD+单补片法 | PDA离断+肺动脉吊带纠治 | 心电图:P-R间期延长 | 心电图正常 |
例7 | LSPV-LINV-SVC | 暂未手术 | / | / | / |
例8 | LSPV-LINV-SVC | 结扎VV+VV与左心耳吻合 | 无 | 室性期前收缩(与术前相仿) | 室性期前收缩增多行射频手术 |
例9 | RIPV-IVC-RA | 人造ASD+双补片法 | 膈肌成形术 | 心电图:P-R间期延长 | 心电图正常 |
例10 | LSPV-LINV-SVC | 结扎VV+VV与左心耳吻合 | 肺动脉狭窄纠治 | 肺动脉流速快(2.0 m·s-1) | 肺动脉流速快(2.0 m·s-1) |
例11 | LSPV-LINV-SVC | 结扎VV+VV与左心耳吻合 | 无 | 心电图:T波改变 | 心电图正常 |
例12 | LSPV+LIPV-LINV-SVC | 结扎VV+VV与左心耳吻合 | 隔离肺切除术 | 心电图:P-R间期延长 | 心电图正常 |
例13 | RIPV-IVC-RA | 人造ASD+双补片法 | 无 | 心电图:T波改变 | 心电图正常 |
例14 | RIPV-IVC-RA | 人造ASD+双补片法 | 无 | 无殊 | 无殊 |
例15 | LSPV-LINV-SVC | 暂未手术 | / | / | / |
例16 | RIPV-RA | 人造ASD+单补片法 | 无 | 心电图:T波改变 | 心电图正常 |
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