Abstract: 　Objective　To explore the endovascular treatment of Budd-Chiari syndrome (BCS) in young child. Methods　The clinical data of one young child diagnosed with BCS and treated with endovascular therapy were retrospectively analyzed. Results　The 23-month-old female suffered from repeated abdominal distension for 3 months and was diagnosed with BCS by vascular ultrasound Doppler and magnetic resonance examination. After confirmation of the diagnosis, endovascular treatment was performed. Then the occluded blood vessels resumed blood stream, urine output increased, and abdominal distension was significant relieved. Conclusions　In young children, BCS is rare, the condition is complex, and endovascular therapy is effective.