目的　探讨新生儿不完全川崎病的临床表现、诊断和治疗。方法　回顾分析1例新生儿不完全川崎病的诊治 过程，并复习相关文献。结果　患儿，男，出生第26天出现持续发热伴皮疹，抗感染治疗无效；首次冠状动脉超声检查无 异常，出现指端脱皮后复查超声证实左侧冠状动脉扩张。经丙种球蛋白及阿司匹林治疗，患儿发热、皮疹好转， 3个月后复 查左侧扩张的冠状动脉恢复正常。随访6个月、 1年及3年，冠状动脉大小及相应指标正常。结论　新生儿川崎病少见，且 表现不典型。

　Objective　To explore the clinical features, diagnosis, and treatment of Kawasaki disease in neonates. Methods　The diagnosis and treatment of incomplete Kawasaki disease in one case were retrospectively analyzed. The related literatures were reviewed. Results　Male infant had persistent fever with rash at 26 days after birth. The anti-infective treatment was ineffective. No abnormality was found in the first coronary artery ultrasonography. However, coronary artery dilatation was confirmed by ultrasonography after skin peeling at fingertips. After the treatment of gamma globulin and aspirin, the symptoms of fever and rash were improved. The left dilated coronary artery returned to normal after 3 month. The size of coronary artery and the corresponding indexes were normal in 6-months, 1-year and 3 year follow-ups. Conclusion　Neonatal Kawasaki disease is rare and atypical.